|Number 08-14 Erdheim-Chester Disease by CMR|
Number 08-14 Erdheim-Chester Disease by CMR
Case from: Patricia Mergo, Mohammed Tabesh, Carsten Schmalfuss, Gary Cooper. Cardiac MRI Unit, University of Florida
History: 41 year old black female admitted for chest pain, malaise, weakness and increasing peripheral edema. Tibial biopsy had demonstrated typical findings of Erdheim-Chester disease (ECD) 8 years earlier. She has previously documented involvement of the long bones, pancreas, pericardium and thoracic aorta with her ECD. Cardiac biomarkers were negative for myocardial necrosis.
CMR Findings: Cines show extensive infiltration and thickening of the pericardium, and a large loculated pericardial fluid collection. There is a mild septal “bounce”. Axial T1 images with and without Fat Sat show infiltration of the interatrial-septum, mild changes in the lung parenchyma and “wrapping” of the aorta. The pericardium enhances after gadolinium (not from fat).