|Number 08-17 Isolated Left Ventricular Apical Hypoplasia.|
Number 08-17 Isolated Left Ventricular Apical Hypoplasia.
Case from: Enrico Franzi’, Giuseppe Leonardi. Department of Cardiology “San Vincenzo” Hospital, Taormina, Italy. Department of Cardiac Surgery “Ferrarotto” Hospital, Catania , Italy .
Clinical History: 35yr male. Known previous DCM diagnosed via echocardiography. Currently stable, NYHA Class I, and well controlled. No significant arrhythmias noted. Referred for CMR.
CMR perspective: These are all features of Isolated Left Ventricular Apical Hypoplasia (ILVAH). A rare congenital cardiomyopathy previously described in 2004 and in the newborn in 2007. The natural progression of this disease is currently not known.